引用本文:陈伟玉,温露华,邓富强,杨海.儿童节段性结肠神经节细胞减少症1例并文献学习[J].中国临床新医学,0,():-.
.儿童节段性结肠神经节细胞减少症1例并文献学习[J].中国临床新医学,0,():-.
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儿童节段性结肠神经节细胞减少症1例并文献学习
陈伟玉,温露华,邓富强,杨海
梅州市人民医院
摘要:
目的:总结儿童节段性结肠神经节细胞减少症(Hypoganglionosis)的临床特点。方法:收集梅州市人民医院小儿外科收治的1例节段性结肠神经节细胞减少症患儿的临床资料并进行回顾性分析总结及文献学习。结果:患者行非拖出式结肠大部分切除、直肠-升结肠吻合术,术后追踪随访半年排便规律,无污粪,半年体重增加4Kg。结论:当节段性结肠神经节细胞减少症病变结肠广泛,直肠活检有正常神经节细胞时,可行非拖出式结肠大部分切除、直肠-升结肠吻合术可获得满意预后。
关键词:  儿童  巨结肠同源病  结肠神经节细胞减少症  手术治疗  病例报告
DOI：
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基金项目:梅州市社会发展科技计划项目（编号：221208152057133）
A CASE REPORT OF SEGMENTAL COLONIC HYPOGANGLIONOSIS IN CHILDREN AND LITERATURE REVIEW
1.Meizhou People'2.'3.s Hospital;1.Meizhou People'2.'3.s Hospital
Abstract:
Objective：Summary of the clinical features of segmental colonic hypoganglionosis in children. Methods：The clinical data of a child with segmental colonic hypoganglionosis admitted to the Pediatric Surgery Department of Meizhou People’s Hospital were collected and retrospectively analyzed and summarized and literature review. Results:The patient underwent non-drag-out subtotal colon resection and recto-ascending colon anastomosis. The patient was followed up for six months after the operation, with no defecation patterns and no dirty feces, and a weight gain of 4Kg in half a year. Conclusion: When the disease of segmental colonic hypoganglionosis is extensive in the colon and normal ganglion cells are found in rectal biopsy, non-pull-out subtotal colon resection and recto-ascending colon anastomosis can be performed to obtain a satisfactory prognosis.
Key words:  Children  Hirschsprung disease allied disorder  Segmental colonic hypoganglionosis  Surgical treatment  Case report